Echocardiography in Pediatric and Congenital Heart Disease

Second Edition

Edited by: Wyman W. Lai, Luc L. Mertens, Meryl S. Cohen, Tal Geva

Echocardiography in Pediatric and Congenital Heart Disease Second Edition Book Cover

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Video 29.9 Heterotaxy syndrome with cardiovascular findings most consistent with polysplenia

Heterotaxy syndrome with cardiovascular findings most consistent with polysplenia. Polysplenia syndrome with common atrium and partial atrioventricular canal {A,D,S} in the setting of mesocardia and abdominal visceral situs ambiguus. There is second-degree heart block with 2:1 atrioventricular conduction and ventricular rates of 50�55 bpm.

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