Video 29.10 Fetal heterotaxy syndrome with total anomalous pulmonary venous connections (TAPVC)
Fetal heterotaxy syndrome with total anomalous pulmonary venous connections (TAPVC). Fetal echocardiogram at 26 weeks’ gestation. The individual pulmonary veins form a confluence behind the left atrium and drain via a vertical vein to the left superior vena cava. In addition to TAPVC, this fetus was diagnosed with levocardia with abdominal visceral situs inversus, tricuspid atresia (segmental set {I,D,D}), large conoventricular septal defect, pulmonary atresia, hypoplastic RV (HRV), and systemic venous anomalies (left-sided intact inferior vena cava and bilateral superior venae cavae).