Video 29.9 Heterotaxy syndrome with cardiovascular findings most consistent with polysplenia
Heterotaxy syndrome with cardiovascular findings most consistent with polysplenia. Polysplenia syndrome with common atrium and partial atrioventricular canal {A,D,S} in the setting of mesocardia and abdominal visceral situs ambiguus. There is second-degree heart block with 2:1 atrioventricular conduction and ventricular rates of 50–55 bpm.